Gaois

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  1. SOCIAL QUESTIONS|health|medical science

    #630282

    IATE #1532427
    siondróm Papillon Lefèvre Reference Faomhadh an téarma seo mar chuid de Thionscadal Lex
    ga
    Keratodermie Typ Papillon Lefèvre | Papillon-Lefèvre-Syndrom
    de
    Definition Keratosis palmoplantaris mit Periodontopathie Reference Reallex Med
    Papillon Lefèvre syndrome
    en
    Definition an extremely rare genodermatosis inherited as an autosomal recessive trait, affecting children between the ages 1-4 years. The disorder is characterized by diffuse palmoplantar keratoderma, which typically has its onset between the ages 1 and 4 years, by premature loss of both deciduous and permanent teeth as well as by severe periodontitis, which starts at age 3 or 4 years. Reference "Based on: Shahbaz A Janjua, Amor Khachemoune. Papillon-Lefèvre syndrome: Case report and review of the literature. Dermatology Online Journal. Volume 10 Number 1 http://dermatology.cdlib.org/101/case_reports/papillon/khachemoune.html [8.3.2010]"
    Comment "For more information, see: Shahbaz A Janjua, Amor Khachemoune. Papillon-Lefèvre syndrome: Case report and review of the literature. Dermatology Online Journal. Volume 10 Number 1 http://dermatology.cdlib.org/101/case_reports/papillon/khachemoune.html [8.3.2010]"
    kératodermie type Papillon Lefèvre
    fr